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Mounier Kuhn Syndrome


Abstract


Mounier Kuhn syndrome or tracheobronchomegaly is characterized by a marked dilatation of the trachea and main bronchi that can extend to the periphery of the lungs. Dilation is due to an alteration of the cartilaginous and membranous structure of the trachea and bronchi. It is a pathology much more frequent in men. The aetiology is unclear. The clinical case in question concerns a 67-year-old man who has reported recurrent episodes of bronchopulmonary infections and hemoptysis, after undergoing instrumental investigations (fibrobroncoscopy and chest CT), the diagnosis of Tracheobroncomegalia or Mounier Kuhn syndrome was formulated.

Keywords: Tracheobroncomegalia; bronchiectasis; diverticula; clearance; chronic inflammation; atrophy; connective tissue disorders (Ehlers-Danlos syndrome and Marfan syndrome)

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